Gorlin-Goltz Syndrome: Report of 4 Cases
Published: 2020-11-07
Page: 175-182
Issue: 2020 - Volume 3 [Issue 1]
Ouassime Kerdoud *
Department of Stomatology, Oral and Maxillofacial Surgery, Hospital of August 20th, University Hospital, Casablanca, Morocco.
Faical Slimani
Department of Stomatology, Oral and Maxillofacial Surgery, Hospital of August 20th, University Hospital, Casablanca, Morocco. and Faculty of Medicine and Pharmacy, Hassan 2 University of Casablanca, Casablanca, Morocco.
*Author to whom correspondence should be addressed.
Abstract
Gorlin-Goltz syndrome, also known as basal cell nevomatosis (CBN), is a rare inherited disorder belonging to the family of neurocristopathies or diseases caused by abnormalities of the neural ridges. We report the case of 4 patients, suffering from this syndrome, followed up in the stomatology and maxillofacial surgery service in Casablanca, including a familial form in two cases: a mother and her son and 2 isolated cases, followed and treated in our service of maxillofacial surgery of the August 20 hospital in Casablanca. A clinical, biological and radiological assessment was made followed by surgical treatment for the 3 patients, an anatomo-pathological examination and the establishment of a strict monitoring plan.
Keywords: Gorlin-Goltz syndrome, cell nevomatosis, stomatology, maxillofacial surgery.